Biventricular myocardial noncompaction presenting with complete atrioventricular block


Yildiz A., Özeke O., Akyol S., Demirbag R., Yilmaz R., Gur M.

INTERNATIONAL JOURNAL OF CARDIOLOGY, cilt.132, sa.1, 2009 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Kısa Makale
  • Cilt numarası: 132 Sayı: 1
  • Basım Tarihi: 2009
  • Doi Numarası: 10.1016/j.ijcard.2007.07.122
  • Dergi Adı: INTERNATIONAL JOURNAL OF CARDIOLOGY
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Anahtar Kelimeler: Aortic insufficiency, Biventricular noncompaction, Complete atrioventricular block, Mitral insufficiency, LEFT-VENTRICULAR MYOCARDIUM
  • Akdeniz Üniversitesi Adresli: Hayır

Özet

Noncompaction of ventricular myocardium has been recognized as a distinct form of cardiomyopathy with its own clinical presentation and natural history. Concomitance of either valvular pathologies or complete atrioventricular block with noncompaction of ventricular myocardium has rarely been reported. Herein, we present a case with biventricular noncompaction with significant interventricular septum involvement presenting with complete atrioventricular block, who was formerly diagnosed to have mitral and aortic insufficiency. (c) 2007 Elsevier Ireland Ltd. All rights reserved.