Facial nerve palsy is a rare neurologic manifestation of Kawasaki disease. There are several mechanisms in the pathogenesis of facial nerve palsy. It is usually transient and lasts for 1 to 90 days. Under normal conditions it resolves spontaneously and completely. Presence of facial paralysis indicates an increased risk of coronary artery aneurism. In this report, a ten month-old girl with prolonged fever, aseptic meningitis and facial palsy who later diagnosed as Kawasaki disease was described and also the clinical features of 37 cases in the literature were reviewed.