Comprehensive dental management in a Hallermann-Streiff syndrome patient with unusual radiographic appearance of teeth
NIGERIAN JOURNAL OF CLINICAL PRACTICE, cilt.18, sa.4, ss.559-562, 2015 (SCI-Expanded, Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 18 Sayı: 4
- Basım Tarihi: 2015
- Doi Numarası: 10.4103/1119-3077.156910
- Dergi Adı: NIGERIAN JOURNAL OF CLINICAL PRACTICE
- Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
- Sayfa Sayıları: ss.559-562
- Anahtar Kelimeler: Dental anomalies, Hallermann-Streiff syndrome, orofacial characteristics
- Akdeniz Üniversitesi Adresli: Evet
Özet
Hallermann-Streiff syndrome (HSS) is a genetic disorder characterized by proportionate dwarfism, birdlike facies, hypotrichosis, skin atrophy, dyscephaly, bilateral microphthalmia, congenital cataracts, a narrow, weak, beaked nose, a hypoplastic mandible, and orodental anomalies. Occurrence is sporadic and distinct patterns of inheritance have not been found. This case report describes the dental management of a 3-year-old girl patient with HSS, who had unusual radiographic appearance of teeth. Furthermore, dental treatments and a 30-month follow-up period of the patient with this rare tooth structure malformation have been presented.