Dental treatment of a patient with Rubinstein Taybi syndrome under sedation

Babun H., Oluş F.

TAOMS 2022, Antalya, Türkiye, 6 - 10 Kasım 2022, ss.138

  • Yayın Türü: Bildiri / Özet Bildiri
  • Basıldığı Şehir: Antalya
  • Basıldığı Ülke: Türkiye
  • Sayfa Sayıları: ss.138
  • Akdeniz Üniversitesi Adresli: Evet

Özet

Introduction: Rubinstein-Taybi Syndrome (RTS) is a rare autosomal dominant syndrome characterized by physical changes such as wide thumbs, large and wide feet, short stature and craniofacial abnormalities, and mental retardation. Case: In terms of anaesthesia, difficult airway, aspiration pneumonia and cardiovascular dysfunction are the conditions that need special attention. Typical dysmorphic facial features such as micrognathia, retrognathia, wide nasal bridge, narrow and hollow palate, hypoplastic maxilla and small mouth are among the most important causes of difficult airway in RTS. Approximately one-third of patients have congenital heart diseases. Recurrent respiratory tract infections may occur in RTS due to microaspiration or gastroesophageal reflux. In this case report, we discussed the dental treatment of a child with RTS under sedation.