Pseudoxanthoma Elasticum with Mallory-Weiss Syndrome: Case Report

PAKSOY TURKOZ F., Ulas T., Bes C., Ozkan K., SAKIZ D., DAL M. S., ...Daha Fazla

TURKIYE KLINIKLERI TIP BILIMLERI DERGISI, cilt.32, sa.3, ss.887-890, 2012 (SCI-Expanded) identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 32 Sayı: 3
  • Basım Tarihi: 2012
  • Doi Numarası: 10.5336/medsci.2010-22259
  • Dergi Adı: TURKIYE KLINIKLERI TIP BILIMLERI DERGISI
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.887-890
  • Anahtar Kelimeler: Elastic tissue, Mallory-Weiss syndrome, gastrointestinal hemorrhage, UPDATE
  • Akdeniz Üniversitesi Adresli: Hayır

Özet

Pseudoxanthoma elasticum is a multi-systemic, genetic disorder of the connective tissue characterized by progressive calcification and fragmentation of elastic fibers in skin, retina, gastrointestinal and cardiovascular systems. Skin changes generally manifest in adulthood and rarely in childhood. Upper gastrointestinal hemorrhage occurs in some cases and is frequently resistant to nonsurgical methods of treatment. As the prognosis of pseudoxanthoma elasticum is related to the involvement of extracutaneous organs, early recognition of the disease is important to take preventive measures and to decrease the morbidity. Herein, we presented a case of pseudoxanthoma elasticum with Mallory-Weiss syndrome, who had repetitive and massive upper gastrointestinal bleeding. To our knowledge, there is no reported case of pseudoxanthoma elasticum with Mallory-Weiss syndrome in the literature.