Spontaneous pneumothorax in Wegener's granulomatosis: a case report

SEZER İ., KOCABAS H., ALKAN MELİKOĞLU M., BUDAK B. S., ÖZBUDAK İ. H., BÜTÜN B.

MODERN RHEUMATOLOGY, vol.18, no.1, pp.76-80, 2008 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 18 Issue: 1
  • Publication Date: 2008
  • Doi Number: 10.1007/s10165-007-0007-y
  • Journal Name: MODERN RHEUMATOLOGY
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.76-80
  • Keywords: Wegener's granulomatosis, Pneumothorax, Musculoskeletal involvement, CYCLOPHOSPHAMIDE
  • Akdeniz University Affiliated: Yes

Abstract

Wegener's granulomatosis (WG) is a multiorgan system disease of unknown etiology characterized by granulomatous inflammation, tissue necrosis, and variable degrees of vasculitis in small- and medium-sized blood vessels. In patients with WG, the musculoskeletal system can be involved before other typical symptoms of the disease. Also in WG, pneumothorax can develop as a rare complication. In this paper, we report a case with WG who had early articular involvement in the absence of classic features of illness and had pneumothorax which resulted from the rupture of the sub-pleural nodule. The aim of this work is to increase the awareness of early articular involvement in WG and the pneumothorax possibility especially in cases with cavitated nodules closure to pleura. This case emphasizes that early diagnosis and treatment is very important in avoiding further complications.