Progressive Familial Intrahepatic Cholestasis in a Newborn Treated with Liver Transplantation
ERCIYES MEDICAL JOURNAL, vol.44, no.2, pp.232-234, 2022 (ESCI, TRDizin)
- Publication Type: Article / Article
- Volume: 44 Issue: 2
- Publication Date: 2022
- Doi Number: 10.14744/etd.2021.48753
- Journal Name: ERCIYES MEDICAL JOURNAL
- Journal Indexes: Emerging Sources Citation Index (ESCI), Academic Search Premier, CAB Abstracts, EMBASE, Veterinary Science Database, Directory of Open Access Journals, TR DİZİN (ULAKBİM)
- Page Numbers: pp.232-234
- Keywords: Cholestasis, liver transplantation, newborn
- Open Archive Collection: AVESIS Open Access Collection
- Akdeniz University Affiliated: Yes
Abstract
Background: Progressive familial intrahepatic cholestasis (PFIC) is a severe cholestatic liver disease often requiring a liver transplant (LT). This report describes PFIC in a newborn with jaundice and hepatosplenomegaly treated with LT in the neonatal period.