An uncommon association relating to cloacal maldevelopment: Bladder agenesis, anorectal atresia, and absence of vulva, vagina, and uterus

KARAGUZEL G., Aslan A., MELIKOGLU M.

JOURNAL OF PEDIATRIC SURGERY, cilt.34, sa.4, ss.612-614, 1999 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 34 Sayı: 4
  • Basım Tarihi: 1999
  • Doi Numarası: 10.1016/s0022-3468(99)90086-6
  • Dergi Adı: JOURNAL OF PEDIATRIC SURGERY
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.612-614
  • Anahtar Kelimeler: agenesis of urinary bladder, ectopic ureter, absence of uterus, vaginal agenesis, cloacal abnormalities
  • Akdeniz Üniversitesi Adresli: Evet

Özet

The authors report on a newborn girl with complex urogenital and hindgut abnormalities. Urogenital anomalies consisted of absence of vulva and vagina, uterine and urethral atresias, bladder agenesis with ectopic ureteric opening, and bilateral pelvic ectopic kidneys. In addition, the baby had anorectal atresia without fistula as a hindgut anomaly. Herein, clinical evaluation and embryological review are made to explain the concomitant occurrence of these rare malformations. Copyright (C) 1999 by W.B. Saunders Company.