Comprehensive dental management in a Hallermann-Streiff syndrome patient with unusual radiographic appearance of teeth

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Güngör Ö., Nur B., Yalcin H., Karayılmaz H., Mihchi E.

NIGERIAN JOURNAL OF CLINICAL PRACTICE, cilt.18, sa.4, ss.559-562, 2015 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 18 Sayı: 4
  • Basım Tarihi: 2015
  • Doi Numarası: 10.4103/1119-3077.156910
  • Dergi Adı: NIGERIAN JOURNAL OF CLINICAL PRACTICE
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.559-562
  • Anahtar Kelimeler: Dental anomalies, Hallermann-Streiff syndrome, orofacial characteristics
  • Akdeniz Üniversitesi Adresli: Evet

Özet

Hallermann-Streiff syndrome (HSS) is a genetic disorder characterized by proportionate dwarfism, birdlike facies, hypotrichosis, skin atrophy, dyscephaly, bilateral microphthalmia, congenital cataracts, a narrow, weak, beaked nose, a hypoplastic mandible, and orodental anomalies. Occurrence is sporadic and distinct patterns of inheritance have not been found. This case report describes the dental management of a 3-year-old girl patient with HSS, who had unusual radiographic appearance of teeth. Furthermore, dental treatments and a 30-month follow-up period of the patient with this rare tooth structure malformation have been presented.