Progressive Familial Intrahepatic Cholestasis in a Newborn Treated with Liver Transplantation

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Acarbulut İ., Sağlam C., Ongun H., Çelik K., Oygur N.

ERCIYES MEDICAL JOURNAL, cilt.44, sa.2, ss.232-234, 2022 (ESCI) identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 44 Sayı: 2
  • Basım Tarihi: 2022
  • Doi Numarası: 10.14744/etd.2021.48753
  • Dergi Adı: ERCIYES MEDICAL JOURNAL
  • Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), Academic Search Premier, CAB Abstracts, EMBASE, Veterinary Science Database, Directory of Open Access Journals, TR DİZİN (ULAKBİM)
  • Sayfa Sayıları: ss.232-234
  • Anahtar Kelimeler: Cholestasis, liver transplantation, newborn
  • Akdeniz Üniversitesi Adresli: Evet

Özet

Background: Progressive familial intrahepatic cholestasis (PFIC) is a severe cholestatic liver disease often requiring a liver transplant (LT). This report describes PFIC in a newborn with jaundice and hepatosplenomegaly treated with LT in the neonatal period.